ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 9  /  I26-I28

Pulmonary heart disease and diseases of pulmonary circulation (I26-I28)

I26 Pulmonary embolism
Includes pulmonary (acute) (artery)(vein) infarction
pulmonary (acute) (artery)(vein) thromboembolism
pulmonary (acute) (artery)(vein) thrombosis
Excludes1 cor pulmonale without embolism (I27.81)
Excludes2 chronic pulmonary embolism (I27.82)
personal history of pulmonary embolism (Z86.711)
pulmonary embolism complicating abortion, ectopic or molar pregnancy (O00-O07, O08.2)
pulmonary embolism complicating pregnancy, childbirth and the puerperium (O88.-)
pulmonary embolism due to trauma (T79.0, T79.1)
pulmonary embolism due to complications of surgical and medical care (T80.0, T81.7-, T82.8-)
septic (non-pulmonary) arterial embolism (I76)
I26.0 Pulmonary embolism with acute cor pulmonale
I26.01 Septic pulmonary embolism with acute cor pulmonale
CodeFirst underlying infection
nonPrimary Yes
I26.02 Saddle embolus of pulmonary artery with acute cor pulmonale
I26.09 Other pulmonary embolism with acute cor pulmonale
Acute cor pulmonale NOS
I26.9 Pulmonary embolism without acute cor pulmonale
I26.90 Septic pulmonary embolism without acute cor pulmonale
CodeFirst underlying infection
nonPrimary Yes
I26.92 Saddle embolus of pulmonary artery without acute cor pulmonale
I26.93 Single subsegmental pulmonary embolism without acute cor pulmonale
Subsegmental pulmonary embolism NOS
I26.94 Multiple subsegmental pulmonary emboli without acute cor pulmonale
I26.99 Other pulmonary embolism without acute cor pulmonale
Acute pulmonary embolism NOS
Pulmonary embolism NOS
I27 Other pulmonary heart diseases
I27.0 Primary pulmonary hypertension
Heritable pulmonary arterial hypertension
Idiopathic pulmonary arterial hypertension
Primary group 1 pulmonary hypertension
Primary pulmonary arterial hypertension
Excludes1 persistent pulmonary hypertension of newborn (P29.30)
pulmonary hypertension NOS (I27.20)
secondary pulmonary arterial hypertension (I27.21)
secondary pulmonary hypertension (I27.29)
I27.1 Kyphoscoliotic heart disease
I27.2 Other secondary pulmonary hypertension
CodeAlso associated underlying condition
Excludes1 Eisenmenger's syndrome (I27.83)
I27.20 Pulmonary hypertension, unspecified
Pulmonary hypertension NOS
I27.21 Secondary pulmonary arterial hypertension
(Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
(Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension
CodeAlso associated conditions if applicable, or adverse effects of drugs or toxins, such as:
adverse effect of appetite depressants (T50.5X5)
congenital heart disease (Q20-Q28)
human immunodeficiency virus [HIV] disease (B20)
polymyositis (M33.2-)
portal hypertension (K76.6)
rheumatoid arthritis (M05.-)
schistosomiasis (B65.-)
Sjögren syndrome (M35.0-)
systemic sclerosis (M34.-)
I27.22 Pulmonary hypertension due to left heart disease
Group 2 pulmonary hypertension
CodeAlso associated left heart disease, if known, such as:
multiple valve disease (I08.-)
rheumatic mitral valve diseases (I05.-)
rheumatic aortic valve diseases (I06.-)
I27.23 Pulmonary hypertension due to lung diseases and hypoxia
Group 3 pulmonary hypertension
CodeAlso associated lung disease, if known, such as:
bronchiectasis (J47.-)
cystic fibrosis with pulmonary manifestations (E84.0)
interstitial lung disease (J84.-)
pleural effusion (J90)
sleep apnea (G47.3-)
I27.24 Chronic thromboembolic pulmonary hypertension
Group 4 pulmonary hypertension
CodeAlso associated pulmonary embolism, if applicable (I26.-, I27.82)
I27.29 Other secondary pulmonary hypertension
Group 5 pulmonary hypertension
Pulmonary hypertension with unclear multifactorial mechanisms
Pulmonary hypertension due to hematologic disorders
Pulmonary hypertension due to metabolic disorders
Pulmonary hypertension due to other systemic disorders
CodeAlso other associated disorders, if known, such as:
chronic myeloid leukemia (C92.10-C92.22)
essential thrombocythemia (D47.3)
Gaucher disease (E75.22)
hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
hyperthyroidism (E05.-)
hypothyroidism (E00-E03)
polycythemia vera (D45)
sarcoidosis (D86.-)
I27.8 Other specified pulmonary heart diseases
I27.81 Cor pulmonale (chronic)
Cor pulmonale NOS
CodeAlso , if applicable, right heart failure (I50.81-)
Excludes1 acute cor pulmonale (I26.0-)
I27.82 Chronic pulmonary embolism
UseAdditionalCode code, if applicable, for associated long-term (current) use of anticoagulants (Z79.01)
Excludes1 personal history of pulmonary embolism (Z86.711)
I27.83 Eisenmenger's syndrome
Eisenmenger's complex
(Irreversible) Eisenmenger's disease
Pulmonary hypertension with right to left shunt related to congenital heart disease
CodeAlso underlying heart defect, if known, such as:
atrial septal defect (Q21.1-)
Eisenmenger's defect (Q21.8)
patent ductus arteriosus (Q25.0)
ventricular septal defect (Q21.0)
I27.89 Other specified pulmonary heart diseases
I27.9 Pulmonary heart disease, unspecified
Chronic cardiopulmonary disease
I28 Other diseases of pulmonary vessels
I28.0 Arteriovenous fistula of pulmonary vessels
Excludes1 congenital arteriovenous fistula (Q25.72)
I28.1 Aneurysm of pulmonary artery
Excludes1 congenital aneurysm (Q25.79)
congenital arteriovenous aneurysm (Q25.72)
I28.8 Other diseases of pulmonary vessels
Pulmonary arteritis
Pulmonary endarteritis
Rupture of pulmonary vessels
Stenosis of pulmonary vessels
Stricture of pulmonary vessels
I28.9 Disease of pulmonary vessels, unspecified