D56 |
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Thalassemia |
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| Excludes1 |
sickle-cell thalassemia (D57.4-)
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D56.0 |
 |
Alpha thalassemia |
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| Alpha thalassemia major | | Hemoglobin H Constant Spring | | Hemoglobin H disease | | Hydrops fetalis due to alpha thalassemia | | Severe alpha thalassemia | | Triple gene defect alpha thalassemia |
| UseAdditionalCode |
code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)
|
| Excludes1 |
alpha thalassemia trait or minor (D56.3) asymptomatic alpha thalassemia (D56.3) hydrops fetalis due to isoimmunization (P56.0) hydrops fetalis not due to immune hemolysis (P83.2)
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| |
D56.1 |
 |
Beta thalassemia |
| |
| Beta thalassemia major | | Cooley's anemia | | Homozygous beta thalassemia | | Severe beta thalassemia | | Thalassemia intermedia | | Thalassemia major |
| Excludes1 |
beta thalassemia minor (D56.3) beta thalassemia trait (D56.3) delta-beta thalassemia (D56.2) hemoglobin E-beta thalassemia (D56.5) sickle-cell beta thalassemia (D57.4-)
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| |
D56.2 |
 |
Delta-beta thalassemia |
| |
| Homozygous delta-beta thalassemia |
| Excludes1 |
delta-beta thalassemia minor (D56.3) delta-beta thalassemia trait (D56.3)
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|
|
| |
D56.3 |
 |
Thalassemia minor |
| |
| Alpha thalassemia minor | | Alpha thalassemia silent carrier | | Alpha thalassemia trait | | Beta thalassemia minor | | Beta thalassemia trait | | Delta-beta thalassemia minor | | Delta-beta thalassemia trait | | Thalassemia trait NOS |
| Excludes1 |
alpha thalassemia (D56.0) beta thalassemia (D56.1) delta-beta thalassemia (D56.2) hemoglobin E-beta thalassemia (D56.5) sickle-cell trait (D57.3)
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D56.4 |
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Hereditary persistence of fetal hemoglobin [HPFH] |
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| |
D56.5 |
 |
Hemoglobin E-beta thalassemia |
| |
| Excludes1 |
beta thalassemia (D56.1) beta thalassemia minor (D56.3) beta thalassemia trait (D56.3) delta-beta thalassemia (D56.2) delta-beta thalassemia trait (D56.3) hemoglobin E disease (D58.2) other hemoglobinopathies (D58.2) sickle-cell beta thalassemia (D57.4-)
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D56.8 |
 |
Other thalassemias |
| |
| Dominant thalassemia | | Hemoglobin C thalassemia | | Mixed thalassemia | | Thalassemia with other hemoglobinopathy |
| Excludes1 |
hemoglobin C disease (D58.2) hemoglobin E disease (D58.2) other hemoglobinopathies (D58.2) sickle-cell anemia (D57.-) sickle-cell thalassemia (D57.4-)
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D56.9 |
 |
Thalassemia, unspecified |
| |
| Mediterranean anemia (with other hemoglobinopathy) |
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