ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 6  /  G89-G99  /  G90
G90 Disorders of autonomic nervous system
Excludes1 dysfunction of the autonomic nervous system due to alcohol (G31.2)
G90.0 Idiopathic peripheral autonomic neuropathy
G90.01 Carotid sinus syncope
Carotid sinus syndrome
G90.09 Other idiopathic peripheral autonomic neuropathy
Idiopathic peripheral autonomic neuropathy NOS
G90.1 Familial dysautonomia [Riley-Day]
G90.2 Horner's syndrome
Bernard(-Horner) syndrome
Cervical sympathetic dystrophy or paralysis
G90.3 Multi-system degeneration of the autonomic nervous system
Neurogenic orthostatic hypotension [Shy-Drager]
Excludes1 orthostatic hypotension NOS (I95.1)
G90.4 Autonomic dysreflexia
UseAdditionalCode code to identify the cause, such as:
fecal impaction (K56.41)
pressure ulcer (pressure area) (L89.-)
urinary tract infection (N39.0)
G90.5 Complex regional pain syndrome I (CRPS I)
Reflex sympathetic dystrophy
Excludes1 causalgia of lower limb (G57.7-)
causalgia of upper limb (G56.4-)
complex regional pain syndrome II of lower limb (G57.7-)
complex regional pain syndrome II of upper limb (G56.4-)
G90.50 Complex regional pain syndrome I, unspecified
G90.51 Complex regional pain syndrome I of upper limb
G90.511 Complex regional pain syndrome I of right upper limb
G90.512 Complex regional pain syndrome I of left upper limb
G90.513 Complex regional pain syndrome I of upper limb, bilateral
G90.519 Complex regional pain syndrome I of unspecified upper limb
G90.52 Complex regional pain syndrome I of lower limb
G90.521 Complex regional pain syndrome I of right lower limb
G90.522 Complex regional pain syndrome I of left lower limb
G90.523 Complex regional pain syndrome I of lower limb, bilateral
G90.529 Complex regional pain syndrome I of unspecified lower limb
G90.59 Complex regional pain syndrome I of other specified site
G90.8 Other disorders of autonomic nervous system
G90.9 Disorder of the autonomic nervous system, unspecified
G90.A Postural orthostatic tachycardia syndrome [POTS]
Chronic orthostatic intolerance
Postural tachycardia syndrome
G90.B LMNB1-related autosomal dominant leukodystrophy