ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 17  /  Q50-Q56  /  Q56
Q56 Indeterminate sex and pseudohermaphroditism
Excludes1 46,XX true hermaphrodite (Q99.1)
androgen insensitivity syndrome (E34.5-)
chimera 46,XX/46,XY true hermaphrodite (Q99.0)
female pseudohermaphroditism with adrenocortical disorder (E25.-)
pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99)
pure gonadal dysgenesis (Q99.1)
Q56.0 Hermaphroditism, not elsewhere classified
Ovotestis
Q56.1 Male pseudohermaphroditism, not elsewhere classified
46, XY with streak gonads
Male pseudohermaphroditism NOS
sex Male
Q56.2 Female pseudohermaphroditism, not elsewhere classified
Female pseudohermaphroditism NOS
sex Female
Q56.3 Pseudohermaphroditism, unspecified
Q56.4 Indeterminate sex, unspecified
Ambiguous genitalia