ICD-10-CM Book 2026 Edition

Chapters ICD-10-CM Book Table of Content /
chapter 17 Q00-QA0 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders /
Q80-Q89 Other congenital malformations /
Q89 Other congenital malformations, not elsewhere classified

  Billable ICD-10-CM Code Q89.81
Q89.81
Kabuki syndrome
Kabuki syndrome, type 1, due to KMT2D mutation
Kabuki syndrome, type 2, due to KDM6A mutation
Niikawa-Kuroki syndrome