ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 1  /  A80-A89

Viral and prion infections of the central nervous system (A80-A89)

Excludes1: postpolio syndrome (G14)
sequelae of poliomyelitis (B91)
sequelae of viral encephalitis (B94.1)
A80 Acute poliomyelitis
Excludes1 acute flaccid myelitis (G04.82)
A80.0 Acute paralytic poliomyelitis, vaccine-associated
A80.1 Acute paralytic poliomyelitis, wild virus, imported
A80.2 Acute paralytic poliomyelitis, wild virus, indigenous
A80.3 Acute paralytic poliomyelitis, other and unspecified
A80.30 Acute paralytic poliomyelitis, unspecified
A80.39 Other acute paralytic poliomyelitis
A80.4 Acute nonparalytic poliomyelitis
A80.9 Acute poliomyelitis, unspecified
A81 Atypical virus infections of central nervous system
Includes diseases of the central nervous system caused by prions
UseAdditionalCode code, if applicable, to identify:
dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
mild neurocognitive disorder due to known physiological condition (F06.7-)
A81.0 Creutzfeldt-Jakob disease
A81.00 Creutzfeldt-Jakob disease, unspecified
Jakob-Creutzfeldt disease, unspecified
A81.01 Variant Creutzfeldt-Jakob disease
vCJD
A81.09 Other Creutzfeldt-Jakob disease
CJD
Familial Creutzfeldt-Jakob disease
Iatrogenic Creutzfeldt-Jakob disease
Sporadic Creutzfeldt-Jakob disease
Subacute spongiform encephalopathy (with dementia)
A81.1 Subacute sclerosing panencephalitis
Dawson's inclusion body encephalitis
Van Bogaert's sclerosing leukoencephalopathy
A81.2 Progressive multifocal leukoencephalopathy
Multifocal leukoencephalopathy NOS
A81.8 Other atypical virus infections of central nervous system
A81.81 Kuru
A81.82 Gerstmann-Sträussler-Scheinker syndrome
GSS syndrome
A81.83 Fatal familial insomnia
FFI
A81.89 Other atypical virus infections of central nervous system
A81.9 Atypical virus infection of central nervous system, unspecified
Prion diseases of the central nervous system NOS
A82 Rabies
A82.0 Sylvatic rabies
A82.1 Urban rabies
A82.9 Rabies, unspecified
A83 Mosquito-borne viral encephalitis
Includes mosquito-borne viral meningoencephalitis
Excludes2 Venezuelan equine encephalitis (A92.2)
West Nile fever (A92.3-)
West Nile virus (A92.3-)
A83.0 Japanese encephalitis
A83.1 Western equine encephalitis
A83.2 Eastern equine encephalitis
A83.3 St Louis encephalitis
A83.4 Australian encephalitis
Kunjin virus disease
A83.5 California encephalitis
California meningoencephalitis
La Crosse encephalitis
A83.6 Rocio virus disease
A83.8 Other mosquito-borne viral encephalitis
A83.9 Mosquito-borne viral encephalitis, unspecified
A84 Tick-borne viral encephalitis
Includes tick-borne viral meningoencephalitis
A84.0 Far Eastern tick-borne encephalitis [Russian spring-summer encephalitis]
A84.1 Central European tick-borne encephalitis
A84.8 Other tick-borne viral encephalitis
A84.81 Powassan virus disease
A84.89 Other tick-borne viral encephalitis
Louping ill
CodeFirst , if applicable, transfusion related infection (T80.22-)
A84.9 Tick-borne viral encephalitis, unspecified
A85 Other viral encephalitis, not elsewhere classified
Includes specified viral encephalomyelitis NEC
specified viral meningoencephalitis NEC
Excludes1 encephalitis due to cytomegalovirus (B25.8)
encephalitis due to herpesvirus NEC (B10.0-)
encephalitis due to herpesvirus [herpes simplex] (B00.4)
encephalitis due to measles virus (B05.0)
encephalitis due to mumps virus (B26.2)
encephalitis due to poliomyelitis virus (A80.-)
encephalitis due to zoster (B02.0)
lymphocytic choriomeningitis (A87.2)
myalgic encephalomyelitis (G93.32)
A85.0 Enteroviral encephalitis
Enteroviral encephalomyelitis
A85.1 Adenoviral encephalitis
Adenoviral meningoencephalitis
A85.2 Arthropod-borne viral encephalitis, unspecified
Excludes1 West nile virus with encephalitis (A92.31)
A85.8 Other specified viral encephalitis
Encephalitis lethargica
Von Economo-Cruchet disease
A86 Unspecified viral encephalitis
Viral encephalomyelitis NOS
Viral meningoencephalitis NOS
A87 Viral meningitis
Excludes1 meningitis due to herpesvirus [herpes simplex] (B00.3)
meningitis due to herpesvirus [herpes simplex] (B00.3)
meningitis due to measles virus (B05.1)
meningitis due to mumps virus (B26.1)
meningitis due to poliomyelitis virus (A80.-)
meningitis due to zoster (B02.1)
A87.0 Enteroviral meningitis
Coxsackievirus meningitis
Echovirus meningitis
A87.1 Adenoviral meningitis
A87.2 Lymphocytic choriomeningitis
Lymphocytic meningoencephalitis
A87.8 Other viral meningitis
A87.9 Viral meningitis, unspecified
A88 Other viral infections of central nervous system, not elsewhere classified
Excludes1 viral encephalitis NOS (A86)
viral meningitis NOS (A87.9)
A88.0 Enteroviral exanthematous fever [Boston exanthem]
A88.1 Epidemic vertigo
A88.8 Other specified viral infections of central nervous system
A89 Unspecified viral infection of central nervous system