 M04 |
 |
Autoinflammatory syndromes |
| |
| Excludes2 |
Crohn's disease (K50.-)
|
|
| |
 M04.1 |
|
Periodic fever syndromes |
| |
| Familial Mediterranean fever | | Hyperimmunoglobin D syndrome | | Mevalonate kinase deficiency | | Tumor necrosis factor receptor associated periodic syndrome [TRAPS] |
|
|
| |
| M04.2 |
|
Cryopyrin-associated periodic syndromes |
| |
| Chronic infantile neurological, cutaneous and articular syndrome [CINCA] | | Familial cold autoinflammatory syndrome | | Familial cold urticaria | | Muckle-Wells syndrome | | Neonatal onset multisystemic inflammatory disorder [NOMID] |
|
|
| |
| M04.8 |
|
Other autoinflammatory syndromes |
| |
| Blau syndrome | | Deficiency of interleukin 1 receptor antagonist [DIRA] | | Majeed syndrome | | Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome [PFAPA] | | Pyogenic arthritis, pyoderma gangrenosum, and acne syndrome [PAPA] |
|
|
| |
| M04.9 |
|
Autoinflammatory syndrome, unspecified |
|